Lupus erythematosus tumidus in childhood treated with antimalarials

Autores: Aguirre Lina María, Toro Ana María, Del Río Cobaleda Delsy Yurledy, Ruiz Suárez Ana Cristina

Resumen

Lupus erythematosus tumidus is a rare dermatosis. It is considered a subtype of chronic cutaneous lupus erythematosus of uncertain pathogenesis, favorable prognosis and rare association with systemic lupus erythematosus. Clinically, it manifests as urticarial-like plaques in photo exposed areas, mainly affecting adults, being extremely rare in pediatric age. Herein, we present two cases of six and nine-year-old male patients with clinical and histological cha-racteristics typical of lupus erythematosus tumidus and poor response to first-line treatment (topical, intralesional steroids and topical calcineurin inhibitors); therefore, it was decided to start systemic therapy with antimalarials, obtaining a very good response.

Palabras clave: Cutaneous lupus erythematosus skin abnormalities photosensitivity disorders child antimalarial drugs.

2018-11-05   |   200 visitas   |   Evalua este artículo 0 valoraciones

Vol. 32 Núm.2. Septiembre-Diciembre 2018 Pags. 141-149 CES Medicina 2018; 32(2)